Product Name :
PEX12 Rabbit Polyclonal Antibody
Predicted band size :
Observed band size :
Synonyms:
Peroxisome assembly protein 12 PEX12 antibody Peroxisome assembly protein 12 PAF3 antibody
Function :
This gene belongs to the peroxin-12 family. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS).
Antibody Type:
Rabbit Polyclonal Antibody
Immunogen :
Synthesized peptide derived from human protein . at AA range: 180-260
Species reactivity:
Human, Rat, Mouse
Verify application:
WB
Coupling :
unconjugated
Clone number:
RRID:
Form :
Liquid
Concentration :
1ug/ul
Storage instructions:
Store at +4℃ after thawing.P(t-Bu)3 Pd G4 Order Aliquot store at -20℃ or -80℃.Formula of 364385-54-6 Avoid repeated freeze / thaw cycles.PMID:33387670
Storage buffer solution:
Liquid in PBS containing 50% glycerol, and 0.02% sodium azide.
Subtype:
IgG
Purification method :
Immunogen affinity purified.
ELTSA :
Molecular weight :
39 kDa
Positive control :
Fetal brain,Testis,